Urgent maxillectomy in infants for rare infantile maxillary tumors

Abstract Objective The purpose of this study was to present our experience with definitive surgical management of infants with Melanotic neuroectodermal tumor of infant (MNTI) and epithelioid hemangioendothelioma (EHE). Patients and methods This study included four male infants with histologically p...

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Bibliographic Details
Published in:International journal of pediatric otorhinolaryngology 2011-09, Vol.75 (9), p.1071-1074
Main Authors: Amer, Hazem E, Sharkawy, Asser A, Musad, Ahmed, Tawfik, Ali, Kamal, Alsharawy
Format: Article
Language:English
Subjects:
Biopsy, Needle
Emergency Treatment
Follow-Up Studies
Humans
Immunohistochemistry
Infant
Infant, Newborn
Infantile maxillary tumors
Male
Maxilla - surgery
Maxillary Neoplasms - congenital
Maxillary Neoplasms - diagnostic imaging
Maxillary Neoplasms - pathology
Maxillary Neoplasms - surgery
Neoplasm Invasiveness - pathology
Neoplasm Staging
Neuroectodermal Tumor, Melanotic - congenital
Neuroectodermal Tumor, Melanotic - pathology
Neuroectodermal Tumor, Melanotic - surgery
Oral Surgical Procedures - methods
Otolaryngology
Pediatrics
Rare Diseases
Retrospective Studies
Risk Assessment
Sampling Studies
Tomography, X-Ray Computed - methods
Treatment Outcome
Urgent maxillectomy
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Summary:Abstract Objective The purpose of this study was to present our experience with definitive surgical management of infants with Melanotic neuroectodermal tumor of infant (MNTI) and epithelioid hemangioendothelioma (EHE). Patients and methods This study included four male infants with histologically proven MNTI (three infants) and EHE (one infant). CT scan and MRI were for taken for the patients preoperatively. Surgical intervention was used in all infants. Results This study is a retrospective study that reflects our experience in the last 20 years in maxillectomy in infants. All infants were male with mean age 6 months (2–9 months). Complete resection of the tumor was achieved all infants with no residual or recurrence. Neither chemotherapy nor radiation was used in this study. Conclusions MNTI and EHE are rare tumor of infant. They present as a slow painless hard swelling of the maxilla. Imaging is an essential before surgical treatment. Complete excision is curative.
ISSN:0165-5876
1872-8464
DOI:10.1016/j.ijporl.2010.12.012