Neonatal Kasabach-Merritt syndrome healed by complete surgical excision of the angioma

Kasabach-Merritt syndrome is an infrequent combination of a giant hemangioma and severe thrombocytopenia. This syndrome may be life-threatening. There are various but no definitive methods of treatment. We describe here a neonatal case cured by total excision of the tumor. A boy was admitted at birt...

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Bibliographic Details
Published in:Archives de pédiatrie : organe officiel de la Société française de pédiatrie 1998-03, Vol.5 (3), p.295
Main Authors: Velin, P, Dupont, D, Golkar, A, Valla, J S
Format: Article
Language:fre
Subjects:
Anti-Inflammatory Agents, Non-Steroidal - therapeutic use
Aspirin - therapeutic use
Back
Glucocorticoids - therapeutic use
Hemangioma - pathology
Hemangioma - surgery
Humans
Infant, Newborn
Male
Methylprednisolone - therapeutic use
Platelet Aggregation Inhibitors - therapeutic use
Skin Neoplasms - pathology
Skin Neoplasms - surgery
Syndrome
Thrombocytopenia - pathology
Thrombocytopenia - therapy
Ticlopidine - therapeutic use
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Summary:Kasabach-Merritt syndrome is an infrequent combination of a giant hemangioma and severe thrombocytopenia. This syndrome may be life-threatening. There are various but no definitive methods of treatment. We describe here a neonatal case cured by total excision of the tumor. A boy was admitted at birth with a giant hemangioma of the back with thrombocytopenia. Tumor compression, corticosteroids, acetylsalicylic acid and ticlopidine were ineffective. Total surgical excision was performed on day 51, resulting in complete recovery. Total surgical excision of a localized hemangioma in a non-functional area is probably the most appropriate and justified treatment for the Kasabach-Merritt syndrome.
ISSN:0929-693X