Intraabdominal follicular dendritic cell sarcoma: a report of three cases and review of the literature

Follicular dendritic cell sarcoma (FDCS) is a rare neoplasm that originates from follicular dendritic cells in lymphoid follicles. FDCS has been increasingly reported in recent years. However, data on FDCS are mostly based on single case reports or case series and its natural history and standard tr...

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Bibliographic Details
Published in:Tumori 2013-03, Vol.99 (2), p.e65
Main Authors: Urun, Yuksel, Kankaya, Duygu, Koral, Lokman, Yalcin, Bulent, Karabork, Ayca, Ceyhan, Koray, Boruban, Melih Cem, Utkan, Güngör, Demirkazik, Ahmet
Format: Article
Language:English
Subjects:
Abdominal Pain - etiology
Adrenalectomy
Adult
Antineoplastic Combined Chemotherapy Protocols - administration & dosage
Antineoplastic Combined Chemotherapy Protocols - therapeutic use
Biomarkers, Tumor - analysis
Chemotherapy, Adjuvant
Colostomy
Cyclophosphamide - administration & dosage
Dendritic Cell Sarcoma, Follicular - complications
Dendritic Cell Sarcoma, Follicular - diagnosis
Dendritic Cell Sarcoma, Follicular - pathology
Dendritic Cell Sarcoma, Follicular - therapy
Diagnosis, Differential
Epirubicin - administration & dosage
Female
Gastrointestinal Stromal Tumors - chemistry
Gastrointestinal Stromal Tumors - complications
Gastrointestinal Stromal Tumors - diagnosis
Gastrointestinal Stromal Tumors - pathology
Gastrointestinal Stromal Tumors - therapy
Humans
Immunohistochemistry
Immunophenotyping
Liver Neoplasms - chemistry
Liver Neoplasms - complications
Liver Neoplasms - diagnosis
Liver Neoplasms - secondary
Liver Neoplasms - therapy
Male
Melanoma - chemistry
Melanoma - complications
Melanoma - diagnosis
Melanoma - pathology
Melanoma - therapy
Melena - etiology
Middle Aged
Multimodal Imaging
Positron-Emission Tomography
Prednisone - administration & dosage
Proctoscopy
Rectal Neoplasms - chemistry
Rectal Neoplasms - complications
Rectal Neoplasms - diagnosis
Rectal Neoplasms - pathology
Rectal Neoplasms - therapy
Tomography, X-Ray Computed
Vincristine - administration & dosage
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Description
Summary:Follicular dendritic cell sarcoma (FDCS) is a rare neoplasm that originates from follicular dendritic cells in lymphoid follicles. FDCS has been increasingly reported in recent years. However, data on FDCS are mostly based on single case reports or case series and its natural history and standard treatment are not clear. To increase the understanding of this rare disease, we report our experience of three cases of FDCS with an analysis of the morphological and immunophenotypic characteristics, clinical course, treatment options and response to treatment. In addition, we reviewed the literature on FDCS.
ISSN:2038-2529
DOI:10.1700/1283.14210