Leptomeningeal Interfoliar Enhancement on Vessel Wall MR Imaging as a Unique Radiologic Finding of Susac Syndrome

Susac syndrome is a rare disorder affecting the brain, retina, and inner ear, probably triggered by an immune-mediated endotheliopathy. Diagnosis is based on clinical presentation and ancillary test findings (brain MR imaging, fluorescein angiography, and audiometry). Recently, vessel wall MR imagin...

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Bibliographic Details
Published in:American journal of neuroradiology : AJNR 2023-03, Vol.44 (3), p.271-273
Main Authors: Cardozo, P, Marrodán, M, Gilmore, A, Fiol, M P, Chaves, H
Format: Article
Language:English
Subjects:
Adult Brain
Brain - diagnostic imaging
Ear, Inner
Humans
Magnetic Resonance Imaging - methods
Retina
Susac Syndrome - diagnostic imaging
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Summary:Susac syndrome is a rare disorder affecting the brain, retina, and inner ear, probably triggered by an immune-mediated endotheliopathy. Diagnosis is based on clinical presentation and ancillary test findings (brain MR imaging, fluorescein angiography, and audiometry). Recently, vessel wall MR imaging has shown increased sensitivity in the detection of subtle signs of parenchymal, leptomeningeal, and vestibulocochlear enhancement. In this report, we describe a unique finding identified using this technique in a series of 6 patients with Susac syndrome and discuss its potential value for diagnostic work-up and follow-up.
ISSN:0195-6108
1936-959X
DOI:10.3174/ajnr.A7801