Subacute Progressive Severe Ataxic Sensory Neuropathy with Sjögren's Syndrome

We herein report a 79-year-old woman with subacute progressive ataxic sensory neuropathy. The patient's symptoms began with numbness in the lower extremities, which rapidly deteriorated, resulting in gait disturbance and abnormal sensations in the extremities, reaching a peak over a period of a...

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Bibliographic Details
Published in:Internal Medicine 2024/06/01, Vol.63(11), pp.1637-1643
Main Authors: Fujioka, Tomohiro, Kondo, Kimito, Kohara, Nobuo
Format: Article
Language:English
Subjects:
Aged
Ataxia - diagnosis
Ataxia - etiology
Case Report
Diagnosis
Disease Progression
Female
Humans
Immunotherapy
Movement disorders
Nerve conduction
Neuropathy
Paraneoplastic syndrome
Peripheral Nervous System Diseases - complications
Peripheral Nervous System Diseases - diagnosis
Peripheral Nervous System Diseases - etiology
Polyneuropathies - complications
Polyneuropathies - diagnosis
Polyneuropathies - etiology
Polyneuropathy
sensory ataxic polyneuropathy
Severity of Illness Index
Sjogren's syndrome
Sjogren's Syndrome - complications
Sjogren's Syndrome - diagnosis
Sjögren's syndrome
subacute sensory neuropathy
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Summary:We herein report a 79-year-old woman with subacute progressive ataxic sensory neuropathy. The patient's symptoms began with numbness in the lower extremities, which rapidly deteriorated, resulting in gait disturbance and abnormal sensations in the extremities, reaching a peak over a period of approximately two months. Nerve conduction studies revealed pure axonal-type sensory polyneuropathy. The expeditious progression of the disease initially prompted suspicion of Guillain-Barré syndrome or paraneoplastic syndrome. Nevertheless, after comprehensive evaluations, the conclusive diagnosis was confirmed as ataxic sensory neuropathy with Sjögren's syndrome. Intensive immunotherapy was administered; however, it was ineffective in halting disease progression. Consequently, this case underscores the significance of an early comprehensive diagnosis and prompt immunotherapy for ataxic sensory neuropathy associated with Sjögren's syndrome.
ISSN:0918-2918
1349-7235
1349-7235
DOI:10.2169/internalmedicine.2226-23