Left Ventricular Non-compaction Cardiomyopathy: A Report of a Rare Case From Saudi Arabia

Left ventricular non-compaction cardiomyopathy (LVNC) is an unusual congenital heart disease that predominantly affects the heart's left ventricle. This disease is characterized by deep intertrabecular recesses and hypertrabeculations of the myocardial wall that link with the ventricle cavity....

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Bibliographic Details
Published in:Curēus (Palo Alto, CA) CA), 2024-07, Vol.16 (7), p.e64937
Main Authors: Irfan Thalib, Husna, Mehveen, Sayeeda, Khan, Sariya, Haidar, Shyma, Jamal, Ayesha, Shaikh, Ayesha, Alfaqih, Mohammed A, Mansy, Amir A
Format: Article
Language:English
Subjects:
Angina pectoris
Blood tests
Cardiac arrhythmia
Cardiology
Cardiomyopathy
Case reports
Cholesterol
Dyspnea
Ejection fraction
Heart
Internal Medicine
Magnetic resonance imaging
Medical imaging
Morphology
Pathology
Patients
Thromboembolism
Ultrasonic imaging
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Summary:Left ventricular non-compaction cardiomyopathy (LVNC) is an unusual congenital heart disease that predominantly affects the heart's left ventricle. This disease is characterized by deep intertrabecular recesses and hypertrabeculations of the myocardial wall that link with the ventricle cavity. During embryogenesis, the fetal myocardium has to undergo a compaction process, wherein the trabeculated and spongy myocardial tissue compacts into a dense, solid form. An incomplete compaction process results in persistent non-compacted spongy myocardial tissue and trabeculations prominent in the left ventricle. This disease could be marked alone or be present in coexistence with other congenital heart abnormalities. We present a rare case of a 57-year-old Saudi male who presented to the ER with chest pain and dyspnea. Due to severe chest pain, he was admitted to the coronary care unit. On further investigation, an echocardiogram revealed heavy trabeculations in the dilated left ventricle and a reduced ejection fraction. The case was diagnosed as LVNC and possible heart failure. The patient was discharged after he was kept under guideline-directed medical therapy (GDMT) along with certain medications and will be evaluated after six months of GDMT to decide on implantable cardiac resynchronization therapy. Although LVNC is rare, it can lead to severe heart conditions like arrhythmias, thromboembolism, and heart failure.
ISSN:2168-8184
2168-8184
DOI:10.7759/cureus.64937