Pulmonary hypertension associated with primary biliary cirrhosis in the absence of portal hypertension: a case report

Pulmonary hypertension is well described in association with portal hypertension of any cause including end stage primary biliary cirrhosis (PBC). The essential feature of this association is the presence of portosystemic shunting, including surgically created shunts. A patient with primary pulmonar...

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Bibliographic Details
Published in:Gut 1994-02, Vol.35 (2), p.280-282
Main Authors: Yoshida, E M, Erb, S R, Ostrow, D N, Ricci, D R, Scudamore, C H, Fradet, G
Format: Article
Language:English
Subjects:
Adult
Biological and medical sciences
Female
Gastroenterology. Liver. Pancreas. Abdomen
Humans
Hypertension, Pulmonary - complications
Liver Cirrhosis, Biliary - complications
Liver. Biliary tract. Portal circulation. Exocrine pancreas
Medical sciences
Other diseases. Semiology
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Summary:Pulmonary hypertension is well described in association with portal hypertension of any cause including end stage primary biliary cirrhosis (PBC). The essential feature of this association is the presence of portosystemic shunting, including surgically created shunts. A patient with primary pulmonary hypertension and PBC without portal hypertension is reported. This suggests that primary pulmonary hypertension may be associated with PBC in the absence of portal hypertension. Decisions regarding appropriate organ transplantation may depend on whether pulmonary hypertension is primary or secondary to portal hypertension.
ISSN:0017-5749
1468-3288
1458-3288
DOI:10.1136/gut.35.2.280