Coats' syndrome: long term follow up

AIM To increase the understanding of the long term results in pseudo-retinoblastoma eyes with infantile Coats' syndrome. METHODS This study design was a retrospective case review. 10 patients were analysed who were initially referred with a diagnosis of retinoblastoma but had Coats' syndro...

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Bibliographic Details
Published in:British journal of ophthalmology 2000-01, Vol.84 (1), p.37-39
Main Author: Char, Devron H
Format: Article
Language:English
Subjects:
Age
Biological and medical sciences
Child, Preschool
Coats' syndrome
Disease
Female
Follow-Up Studies
Glaucoma
Humans
Infant
Lasers
Lipids
Male
Medical imaging
Medical prognosis
Medical sciences
Ophthalmology
Original articles - Clinical science
Patients
Retina
Retina - diagnostic imaging
Retina - surgery
Retinal Detachment - diagnostic imaging
Retinal Detachment - physiopathology
Retinal Detachment - surgery
Retinopathies
Retrospective Studies
Syndrome
Telangiectasis - diagnostic imaging
Telangiectasis - physiopathology
Telangiectasis - surgery
Tomography, X-Ray Computed
Ultrasonic imaging
Visual Acuity
visual outcome
Young adults
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Summary:AIM To increase the understanding of the long term results in pseudo-retinoblastoma eyes with infantile Coats' syndrome. METHODS This study design was a retrospective case review. 10 patients were analysed who were initially referred with a diagnosis of retinoblastoma but had Coats' syndrome on the basis of ocular oncological evaluation. Vision, fundus photography, ultrasonography, and computed tomography scans were obtained and evaluated. Changes in vision and retinal status were measured. RESULTS The initial age at presentation was 2.4 years (range 0.25–4 years). All patients had retinal detachment at diagnosis. Nine of 10 retinas were reattached after various treatments. Reattached retinas had closure of peripheral telangiectasia and visible intraretinal crystals. Vision was dismal. At last follow up (mean 8.8 years), only two patients had 20/400 or better visual acuities. Five eyes had no light perception despite early treatment to reattach the retina. Nine of 10 eyes remain cosmetically acceptable. One patient wore a cosmetic shell. CONCLUSIONS Long term results indicate that these eyes can be salvaged and the retina reattached but the visual outcome is poor.
ISSN:0007-1161
1468-2079
DOI:10.1136/bjo.84.1.37