Arrhythmogenic right ventricular dysplasia. An illustrated review highlighting developments in the diagnosis and management of this potentially fatal condition

Arrhythmogenic right ventricular dysplasia is an inherited, progressive condition. Characterised by fatty infiltration of the right ventricle, it frequently results in life threatening cardiac arrhythmias, and is one of the important causes of sudden cardiac death in the young. There are characteris...

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Bibliographic Details
Published in:Postgraduate medical journal 2000-07, Vol.76 (897), p.395-398
Main Authors: Fisher, N G, Gilbert, T J
Format: Article
Language:English
Subjects:
Adrenergic beta-Antagonists - therapeutic use
Adult
Amiodarone - therapeutic use
Anti-Arrhythmia Agents - therapeutic use
arrhythmogenic right ventricular dysplasia
Arrhythmogenic Right Ventricular Dysplasia - complications
Arrhythmogenic Right Ventricular Dysplasia - diagnosis
Arrhythmogenic Right Ventricular Dysplasia - therapy
Biological and medical sciences
Bundle-Branch Block - etiology
Cardiac arrhythmia
Catheters
Death, Sudden, Cardiac - etiology
Defibrillators, Implantable
Drug Synergism
Echocardiography
Electrocardiography
Electrocardiography. Vectocardiography
Electrodiagnosis. Electric activity recording
Fatigue - etiology
Heart attacks
Humans
Investigative techniques, diagnostic techniques (general aspects)
Magnetic Resonance Imaging
Male
Medical sciences
Review
Sotalol - therapeutic use
Syncope - etiology
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Description
Summary:Arrhythmogenic right ventricular dysplasia is an inherited, progressive condition. Characterised by fatty infiltration of the right ventricle, it frequently results in life threatening cardiac arrhythmias, and is one of the important causes of sudden cardiac death in the young. There are characteristic electrocardiographic and echocardiographic features that all physicians need to be aware of if we are to reduce these occurrences of premature death. Diagnosis with magnetic resonance imaging is discussed along with current treatment options.
ISSN:0032-5473
1469-0756
DOI:10.1136/pmj.76.897.395