Xanthoma disseminatum with respiratory tract involvement and fatal outcome

Xanthoma disseminatum (XD) is a rare mucocutaneous xanthomatosis classified as a benign form of non-Langerhans' cell histiocytosis. The case history is presented of a 61 year old woman with XD who developed dyspnoea and spirometric features of airflow obstruction. Bronchoscopy and computed tomo...

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Bibliographic Details
Published in:Thorax 2000-02, Vol.55 (2), p.170-172
Main Authors: Davies, Christopher W H, Marren, Pauline, Juniper, Mark C, Gray, Winifred, Wojnorowska, Fenella, Benson, Malcolm K
Format: Article
Language:English
Subjects:
Airway management
Airway Obstruction - etiology
Biological and medical sciences
Biopsy
Bronchoscopy
Case Report
Dyspnea - etiology
Fatal Outcome
Female
Histiocytosis, Non-Langerhans-Cell - complications
Histiocytosis, Non-Langerhans-Cell - pathology
Humans
Larynx
Medical sciences
Microscopy
Middle Aged
Ostomy
respiratory tract
Sarcoidosis. Granulomatous diseases of unproved etiology. Connective tissue diseases. Elastic tissue diseases. Vasculitis
Tomography, X-Ray Computed
xanthoma disseminatum
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Summary:Xanthoma disseminatum (XD) is a rare mucocutaneous xanthomatosis classified as a benign form of non-Langerhans' cell histiocytosis. The case history is presented of a 61 year old woman with XD who developed dyspnoea and spirometric features of airflow obstruction. Bronchoscopy and computed tomography confirmed involvement of the large and medium sized bronchi and she subsequently died from acute respiratory failure. The post-mortem findings and the importance of respiratory tract disease in this unusual condition are discussed.
ISSN:0040-6376
1468-3296
DOI:10.1136/thorax.55.2.170