Pulmonary hypertension associated with non-cirrhotic portal hypertension in systemic lupus erythematosus

A case of non-cirrhotic portal hypertension in a patient with systemic lupus erythematosus, the first of our knowledge, is described. Severe pulmonary hypertension was associated with the portal hypertension and with markers of active auto-immunity. Pulmonary hypertension has not previously been ass...

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Bibliographic Details
Published in:Postgraduate medical journal 1994-01, Vol.70 (819), p.41-43
Main Authors: Woolf, D., Voigt, M. D., Jaskiewicz, K., Kalla, A. A.
Format: Article
Language:English
Subjects:
Adult
Biological and medical sciences
Female
Humans
Hypertension, Portal - complications
Hypertension, Portal - pathology
Hypertension, Pulmonary - complications
Hypertension, Pulmonary - pathology
Liver - pathology
Lupus Erythematosus, Systemic - complications
Lupus Erythematosus, Systemic - pathology
Medical sciences
Sarcoidosis. Granulomatous diseases of unproved etiology. Connective tissue diseases. Elastic tissue diseases. Vasculitis
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Description
Summary:A case of non-cirrhotic portal hypertension in a patient with systemic lupus erythematosus, the first of our knowledge, is described. Severe pulmonary hypertension was associated with the portal hypertension and with markers of active auto-immunity. Pulmonary hypertension has not previously been associated with non-cirrhotic portal hypertension. The coexistence of vasculopathy of the portal and pulmonary vascular beds in this patient with active autoimmunity supports the postulate that portal-pulmonary hypertension may be immunologically mediated.
ISSN:0032-5473
1469-0756
DOI:10.1136/pgmj.70.819.41