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Maffucci'S syndrome associated with hyperparathyroidism

Maffucci's syndrome is a rare, congenital, nonhereditary, mesodermal dysplastic disease characterized by venous malformations and benign cartilaginous tumors. The occurrence of endocrine tumors in Maffucci's syndrome is very rare. We report a case of Maffucci's syndrome associated wit...

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Published in:Indian journal of dermatology 2011-03, Vol.56 (2), p.203-205
Main Authors: Rao, Angoori Gnaneshwar, Indira, Danturty, Rekha, Tulja Narsing
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Language:English
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container_title Indian journal of dermatology
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Indira, Danturty
Rekha, Tulja Narsing
description Maffucci's syndrome is a rare, congenital, nonhereditary, mesodermal dysplastic disease characterized by venous malformations and benign cartilaginous tumors. The occurrence of endocrine tumors in Maffucci's syndrome is very rare. We report a case of Maffucci's syndrome associated with hyperparathyroidism and multinodular goiter.
doi_str_mv 10.4103/0019-5154.80418
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identifier ISSN: 0019-5154
ispartof Indian journal of dermatology, 2011-03, Vol.56 (2), p.203-205
issn 0019-5154
1998-3611
language eng
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source Publicly Available Content Database; DOAJ Directory of Open Access Journals; PubMed Central
subjects Bone density
Care and treatment
Case Report
Case studies
Diagnosis
Diagnosis, Ultrasonic
Disease
Health aspects
Hyperparathyroidism
Pancreas
Patient outcomes
Risk factors
Skin cancer
Tumors
title Maffucci'S syndrome associated with hyperparathyroidism
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