Prevalence of IgG4-Related Disease in Japan Based on Nationwide Survey in 2009

The number of patients with autoimmune pancreatitis who visited hospitals in Japan in 2007 was approximately 2709 (95% confidence interval; range 2540–3040). Because IgG4-related disease is a new clinical entity, there are no data with regard to its prevalence. To estimate the number of patients wit...

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Bibliographic Details
Published in:International Journal of Rheumatology 2012-01, Vol.2012 (2012), p.117-121
Main Authors: Uchida, Kazushige, Masamune, Atsushi, Shimosegawa, Tooru, Okazaki, Kazuichi
Format: Article
Language:English
Subjects:
Age
Confidence intervals
Departments
Epidemiology
Gastroenterology
Hospitals
Internal medicine
Kidney diseases
Medicine
Population
Questionnaires
Rheumatology
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Summary:The number of patients with autoimmune pancreatitis who visited hospitals in Japan in 2007 was approximately 2709 (95% confidence interval; range 2540–3040). Because IgG4-related disease is a new clinical entity, there are no data with regard to its prevalence. To estimate the number of patients with IgG4-related disease in Japan, we randomly selected hospitals using stratification and asked them how many patients they had with IgG4-related disease in 2009. The number of patients with Mikulicz’s disease, IgG4-related retroperitoneal fibrosis, IgG4-related renal disease, IgG4-related pulmonary disease, and IgG4-related lymphadenopathy who visited hospitals in Japan in 2009 was approximately 4304 (95% confidence interval; range 3360–5048), 272 (95% confidence interval; range 264–306), 57 (95% confidence interval; range 47–66), 354 (95% confidence interval; range 283–424), and 203 (95% confidence interval; range 187–240), respectively. The total number of patients with IgG4-related disease without autoimmune pancreatitis in Japan was approximately 5190 (95% confidence interval; range 4141–6084). The male : female ratio was 1 : 0.77, and the average of age of disease onset was 58.8 years. The total number of patients with IgG4-related disease in Japan in 2009, including autoimmune pancreatitis, was approximately 8000.
ISSN:1687-9260
1687-9279
DOI:10.1155/2012/358371