Endodontic management of a patient with Bernard-Soulier syndrome

Bernard-Soulier syndrome is a rare inherited disorder with giant platelets, thrombocytopenia and a prolonged bleeding time. These abnormalities are caused by genetic defects of the glycoprotein Ib/IX/V complex that constitutes the von Willebrand factor receptor on the platelet surface. We are docume...

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Bibliographic Details
Published in:Journal of conservative dentistry 2014-03, Vol.17 (2), p.188-191
Main Authors: Johns, Dexton Antony, Gopalan, Reji P, Kamble, Ganesh Tukaram, Vidyanath, S
Format: Article
Language:English
Subjects:
Blood diseases
Blood platelets
Care and treatment
Case Report
Case studies
Dentistry
Methods
Root canal therapy
Teeth
Tooth diseases
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Summary:Bernard-Soulier syndrome is a rare inherited disorder with giant platelets, thrombocytopenia and a prolonged bleeding time. These abnormalities are caused by genetic defects of the glycoprotein Ib/IX/V complex that constitutes the von Willebrand factor receptor on the platelet surface. We are documenting a 30-year-old female patient reported with a chief complaint of swelling in relation to right maxillary canine for 5 days. The primary treatment remains platelet transfusion. Root canal treatment was performed following platelet rich plasma transfusion. As the tooth was necrotic and had a periapical pathology post-operative bleeding was absent. The root canal treatment was uneventful and the patient was asymptomatic. Optimum oral hygiene practices were emphasized to avoid dental diseases.
ISSN:0972-0707
0974-5203
DOI:10.4103/0972-0707.128044