Liver fibrosis in primary intestinal lymphangiectasia: An undervalued topic

The relationship between primary intestinal lymphangiectasia(PIL) and liver fibrosis is an emerging topic with many obscure aspects due to the rarity of the disorder.A recent paper reported that a six-month lowfat diet improved liver fibrosis.We report the case of a 17-year-old girl affected by PIL...

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Published in:World journal of hepatology 2014-09, Vol.6 (9), p.685-687
Main Authors: Licinio, Raffaele, Principi, Mariabeatrice, Ierardi, Enzo, Di Leo, Alfredo
Format: Article
Language:English
Subjects:
Case Report
diet
elastography
fibrosis
Hepatic
intestinal
Liver
Low-fat
lymphangiectasia
Primary
transient
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description The relationship between primary intestinal lymphangiectasia(PIL) and liver fibrosis is an emerging topic with many obscure aspects due to the rarity of the disorder.A recent paper reported that a six-month lowfat diet improved liver fibrosis.We report the case of a 17-year-old girl affected by PIL whose hepatic fibrosis progressively worsened within one year,despite dietetic support.This and the previous case report describe extraordinary events,which do not allow clear-cut clinical aspects to be established.Nevertheless,both cases suggest that in patients with PIL,it is necessary to closely monitor liver morphology with in-depth investigations including not only ultrasonography,but also elastography.
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subjects Case Report
diet
elastography
fibrosis
Hepatic
intestinal
Liver
Low-fat
lymphangiectasia
Primary
transient
title Liver fibrosis in primary intestinal lymphangiectasia: An undervalued topic
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