Metastatic Intracranial Adenoid Cystic Carcinoma with Unknown Primary: Case Report and Review of Literature

Adenoid cystic carcinoma (ACC) is an epithelial malignancy comprising approximately 8-10% of all salivary gland tumors. Intracranial ACC without a known primary is an extremely rare pathobiological event. Only 13 cases have been reported in available literature. We report a case of a rare intracrani...

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Bibliographic Details
Published in:Journal of neurosciences in rural practice 2017-04, Vol.8 (2), p.274-276
Main Authors: Chaturvedi, Jitender, Konar, Subas Kanti, Jethwani, Dilip, Srinivas, Dwarakanath, Mahadevan, Anita
Format: Article
Language:English
Subjects:
Adenocarcinoma
Cancer
Cancer metastasis
Care and treatment
Case Report
Case reports
Development and progression
Medical prognosis
Radiation therapy
Risk factors
Tumors
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Summary:Adenoid cystic carcinoma (ACC) is an epithelial malignancy comprising approximately 8-10% of all salivary gland tumors. Intracranial ACC without a known primary is an extremely rare pathobiological event. Only 13 cases have been reported in available literature. We report a case of a rare intracranial ACC in a 35-year-old gentleman presenting with features of raised intracranial pressure. Patient had a lesion in the right parieto-occipital lobe and underwent gross total decompression. There was no evidence of any primary after a thorough systemic evaluation. In the postoperative period, he showed a good clinical improvement and was recurrence free at follow-up of 18 months. We also discuss and review the existing relevant literature.
ISSN:0976-3147
0976-3155
DOI:10.4103/0976-3147.203810