Poland syndrome: a case report

Description Poland syndrome (PS) is a rare chest wall developmental anomaly characterised by ipsilateral agenesis/hypoplasia of the sternocostal head of pectoralis major, hypoplasia of nipple or breast, absence of subcutaneous fat, multiple rib abnormalities, elevated and rotated scapula (Sprengel d...

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Bibliographic Details
Published in:BMJ case reports 2017-08, Vol.2017, p.bcr-2017-221564
Main Authors: Bansal, Apurva, Reddy, Keerthi, Dinsmore, Kristen, Gonzalez-Estrada, Alexei
Format: Article
Language:English
Subjects:
Breast cancer
Case reports
Child
Congenital diseases
Diagnosis, Differential
Family medical history
Humans
Images In
Male
Mastectomy
Musculoskeletal diseases
Pediatrics
Poland Syndrome - diagnosis
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Description
Summary:Description Poland syndrome (PS) is a rare chest wall developmental anomaly characterised by ipsilateral agenesis/hypoplasia of the sternocostal head of pectoralis major, hypoplasia of nipple or breast, absence of subcutaneous fat, multiple rib abnormalities, elevated and rotated scapula (Sprengel deformity) and ipsilateral digit abnormalities (brachydactyly, syndactyly). Left-sided PS has been associated with dextrocardia particularly in patients with agenesis of two or more ribs. 2 The 'vascular theory' has been proposed for other variants of this...
ISSN:1757-790X
1757-790X
DOI:10.1136/bcr-2017-221564