Diagnostic imaging and CEUS findings in a rare case of Desmoid-type fibromatosis. A case report

Desmoid-type fibromatosis (DF), also known as aggressive fibromatosis, is a locally aggressive benign fibroblastic neoplasm that can infiltrate or recur but cannot metastasize. It is rare, with an estimated annual incidence of two to four new cases per million people. Most DFs occur sporadically, bu...

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Bibliographic Details
Published in:Journal of ultrasound 2018-09, Vol.21 (3), p.253-257
Main Authors: Valentino, Massimo, Liberatore, Mauro, Maghella, Fabrizio, De Soccio, Valeria, De Felice, Carlo, Messineo, Daniela, Drudi, Francesco Maria
Format: Article
Language:English
Subjects:
Abdominal Neoplasms - diagnostic imaging
Abdominal Neoplasms - pathology
Aged
Case Report
Case reports
Contrast Media
Diagnosis, Differential
Diagnostic systems
Female
Fibromatosis, Abdominal - diagnostic imaging
Fibromatosis, Abdominal - pathology
Fibromatosis, Abdominal - surgery
Fibromatosis, Aggressive - diagnostic imaging
Fibromatosis, Aggressive - pathology
Fibromatosis, Aggressive - surgery
Humans
Magnetic Resonance Imaging
Medical imaging
Medicine
Medicine & Public Health
Microbubbles
Tomography, X-Ray Computed
Ultrasonography
Ultrasound
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Summary:Desmoid-type fibromatosis (DF), also known as aggressive fibromatosis, is a locally aggressive benign fibroblastic neoplasm that can infiltrate or recur but cannot metastasize. It is rare, with an estimated annual incidence of two to four new cases per million people. Most DFs occur sporadically, but it may also be associated with the hereditary syndrome familial adenomatous polyposis. Treatment is necessary when the disease is symptomatic, especially in case of compression of critical structures. When possible, surgical resection is the treatment of choice; however, recurrence is common. Due to the high rate of recurrence, imaging plays an important role not only in diagnosis, but also in the management of DF. Although there are a number of studies describing CT and MRI findings of DF, there is no description of contrast-enhanced ultrasound findings.
ISSN:1876-7931
1971-3495
1876-7931
DOI:10.1007/s40477-018-0291-8