Exudative Retinal Detachment due to Coats Disease in a Teenager with Senior-Loken Syndrome: Case Report and Review of Literature

Senior-Loken syndrome is a rare disorder that presents in the first two decades of life. It commonly manifests with nephronophthisis and retinal dystrophy. We describe a teenager who had end-stage renal failure presenting with bilateral visual impairment due to retinal dystrophy with concomitant uni...

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Bibliographic Details
Published in:Curēus (Palo Alto, CA) CA), 2019-04, Vol.11 (4), p.e4460
Main Authors: Khairil-Ridzwan, Kamalul Khusus, Azian, Adnan, Hanizasurana, Hashim, Shatriah, Ismail
Format: Article
Language:English
Subjects:
Case reports
Cataracts
Cryotherapy
Cysts
Family medical history
Glaucoma
Kidney diseases
Lasers
Nephrology
Ophthalmology
Patients
Pediatrics
Retina
Teenagers
Vascular endothelial growth factor
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Summary:Senior-Loken syndrome is a rare disorder that presents in the first two decades of life. It commonly manifests with nephronophthisis and retinal dystrophy. We describe a teenager who had end-stage renal failure presenting with bilateral visual impairment due to retinal dystrophy with concomitant unilateral Coats disease and exudative retinal detachment. The patient was treated with a combination of endolaser photocoagulation and external drainage of the subretinal fluid. The final visual acuity remained poor in both eyes. Options of treatment in this challenging situation is discussed in this case report.
ISSN:2168-8184
2168-8184
DOI:10.7759/cureus.4460