A Successful Steroid-Sparing Approach in Cronkhite-Canada Syndrome

Cronkhite-Canada Syndrome (CCS) is a rare, sporadic polyposis condition. The literature on CCS consists mostly of case reports. Although disease presentation has been well-described, there is no consensus on the management of CCS. We present a severe case of CCS that demonstrated clinical and endosc...

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Bibliographic Details
Published in:ACG case reports journal 2019-03, Vol.6 (3), p.e00055-e00055
Main Authors: Mao, Eric J., Hyder, Sarah M., DeNucci, Thomas D., Fine, Sean
Format: Article
Language:English
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Case Report
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Summary:Cronkhite-Canada Syndrome (CCS) is a rare, sporadic polyposis condition. The literature on CCS consists mostly of case reports. Although disease presentation has been well-described, there is no consensus on the management of CCS. We present a severe case of CCS that demonstrated clinical and endoscopic response to corticosteroids. This response was maintained with azathioprine. This case provides additional experience on a therapeutic strategy to induce and maintain a durable corticosteroid-free remission.
ISSN:2326-3253
2326-3253
DOI:10.14309/crj.0000000000000055