Interesting pancreatic tumour in the background of Tuberous Sclerosis

Tuberous Sclerosis Complex (TSC) is easily discernible by a myriad of manifestations, most notably dermatological. It is associated with well known and recognised intra-abdominal tumours like angiomyolipoma of the kidney. However, rarer tumours like pancreatic neuroendocrine tumours can occur in the...

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Bibliographic Details
Published in:BMJ case reports 2019-08, Vol.12 (8), p.e227292
Main Authors: Amarjothi, JMV, Jesudason, Jeyasudhahar, Ramasamy, Villalan, Babu, OL Naganath
Format: Article
Language:English
Subjects:
Abdomen
Adolescent
Biopsy
Cancer
Case reports
Cysts
Female
Health surveillance
Humans
Kidneys
Nervous system
Neuroendocrine tumors
Neuroendocrine Tumors - congenital
Pancreas
Pancreatic cancer
Pancreatic Neoplasms - congenital
Patients
Rare Disease
Surgery
Systematic review
Tuberous sclerosis
Tuberous Sclerosis - complications
Young adults
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Summary:Tuberous Sclerosis Complex (TSC) is easily discernible by a myriad of manifestations, most notably dermatological. It is associated with well known and recognised intra-abdominal tumours like angiomyolipoma of the kidney. However, rarer tumours like pancreatic neuroendocrine tumours can occur in the setting of TSC. A high index of suspicion is necessary to identify and treat these lesions early in their natural course. Early identification augurs well with complete surgical excision and excellent survival.
ISSN:1757-790X
1757-790X
DOI:10.1136/bcr-2018-227292