Desmoid Tumor as an Initial Presentation of Familial Adenomatous Polyposis: A Review of the Literature

Desmoid tumors (DTs) are rare soft tissue neoplasms, especially when originating from the small bowel. An association with familial adenomatous polyposis (FAP) of the colon has been well documented. Within the FAP population, there is a strong correlation between prophylactic procto-colectomy and su...

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Bibliographic Details
Published in:Curēus (Palo Alto, CA) CA), 2018-03, Vol.10 (3), p.e2297-e2297
Main Authors: Haddad, Fady G, El Bitar, Sandy, Barakat, Iskandar, Deeb, Liliane
Format: Article
Language:English
Subjects:
Abdomen
Colorectal cancer
Endoscopy
Fibroblasts
Gastroenterology
Genetic disorders
Hospitals
Internal Medicine
Literature reviews
Mesentery
NMR
Nuclear magnetic resonance
Oncology
Polyps
Tumors
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Summary:Desmoid tumors (DTs) are rare soft tissue neoplasms, especially when originating from the small bowel. An association with familial adenomatous polyposis (FAP) of the colon has been well documented. Within the FAP population, there is a strong correlation between prophylactic procto-colectomy and subsequent development of DTs. Very few reports describe cases of FAP initially presenting with desmoid-related complications. Therefore, we underwent a review of the literature in order to delineate the characteristics of desmoid tumors occurring as an initial presentation of FAP.
ISSN:2168-8184
2168-8184
DOI:10.7759/cureus.2297