Multidisciplinary approach in the management of uterine intravenous leiomyomatosis with intracardiac extension: case report and review of literature

Uterine intravenous leiomyomatosis is an uncommon tumor, usually arising from the uterus, with nodular masses which extend intravascularly over variable distances and may reach the inferior vena cava, right atrium, and pulmonary arteries. Early diagnosis and surgical intervention are crucial as intr...

Full description

Saved in:
Bibliographic Details
Published in:Journal of radiology case reports 2019-07, Vol.13 (7), p.1-13
Main Authors: Marrone, Gianluca, Crinò, Francesca, Morsolini, Marco, Caruso, Settimo, Miraglia, Roberto
Format: Article
Language:English
Subjects:
Echocardiography, Doppler
Female
General Radiology
Heart - diagnostic imaging
Heart Neoplasms - complications
Heart Neoplasms - diagnostic imaging
Heart Neoplasms - surgery
Humans
Leiomyomatosis - complications
Leiomyomatosis - diagnostic imaging
Leiomyomatosis - pathology
Leiomyomatosis - surgery
Middle Aged
Neoplasm Invasiveness - diagnostic imaging
Tomography, X-Ray Computed
Ultrasonography, Doppler, Color
Uterine Neoplasms - complications
Uterine Neoplasms - diagnostic imaging
Uterine Neoplasms - surgery
Uterus - diagnostic imaging
Uterus - surgery
Citations: Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Uterine intravenous leiomyomatosis is an uncommon tumor, usually arising from the uterus, with nodular masses which extend intravascularly over variable distances and may reach the inferior vena cava, right atrium, and pulmonary arteries. Early diagnosis and surgical intervention are crucial as intracardiac leiomyomatosis not only causes cardiac symptoms but may result in pulmonary embolism and sudden death. Complete tumor resection is key in disease management, thus rendering cardiac-extending uterine intravenous leiomyomatosis one of the most challenging conditions for surgical treatment. The use of interventional radiology procedures can facilitate the surgical approach. We report the case of a massive pelvic recurrence of uterine leiomyomatosis with intracardiac extension and pulmonary embolism, analyzing management and surgical outcomes, highlighting the role of interventional radiology during the therapeutic pathway. Nonetheless, there are currently very few data available concerning the use of interventional radiology procedures in the therapeutic strategy of uterine intravenous leiomyomatosis with intracardiac extension.
ISSN:1943-0922
1943-0922
DOI:10.3941/jrcr.v13i7.3607