A Fatal Case of Primary Orbital Ewing's Sarcoma with Intracranial Extensions in a Six-year-old Girl

Ewing's sarcoma (ES) is the second most common skeletal tumor seen in children and adolescents which typically involves the long bones and the axial skeleton. ES involving the orbits is extremely rare and can lead to serious consequences. Patients usually present with fever, localized bone pain...

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Bibliographic Details
Published in:Curēus (Palo Alto, CA) CA), 2019-11, Vol.11 (11), p.e6248
Main Authors: Raza, Natasha, Iqbal, Zia, Nasim, Mahwish, Nasir, Saad, Sehar, Alina
Format: Article
Language:English
Subjects:
Biomarkers
Blood pressure
Bone cancer
Case reports
Children & youth
Ewings sarcoma
Health sciences
Histopathology
Hospitals
Medical prognosis
Metastasis
NMR
Nuclear magnetic resonance
Oncology
Orthopedics
Patients
Pediatrics
Tumors
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Summary:Ewing's sarcoma (ES) is the second most common skeletal tumor seen in children and adolescents which typically involves the long bones and the axial skeleton. ES involving the orbits is extremely rare and can lead to serious consequences. Patients usually present with fever, localized bone pain which increases during the night time, and a visible mass, often with a preceding history of trauma. The diagnosis is confirmed with immunohistochemistry. Patient management involves a multidisciplinary approach with complete focal surgical excision of the tumor along with multiple chemotherapeutic agents and radiation therapy.
ISSN:2168-8184
2168-8184
DOI:10.7759/cureus.6248