Is Immunosuppressive and Thrombolytic Therapy Really Effective in a Patient With Intracardiac Thrombosis and Pulmonary Artery Aneurysm due to Behçet’s Disease?

Behcet's disease (BD) is a rare, multisystemic, chronic vasculitic disorder with unknown etiology. Intracardiac thrombus formation and pulmonary artery aneurysm in BD are very rare. The treatment protocol in patients with vascular involvement, particularly those with pulmonary artery aneurysm a...

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Bibliographic Details
Published in:Archives of rheumatology 2019-12, Vol.34 (4), p.451-456
Main Authors: Ciftdemir, Nukhet Aladag, Gokalp, Selman, Eren, Tuba
Format: Article
Language:English
Subjects:
Aneurysms
Blood clot
Care and treatment
Case Report
Children
Development and progression
Health aspects
Thrombosis
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Summary:Behcet's disease (BD) is a rare, multisystemic, chronic vasculitic disorder with unknown etiology. Intracardiac thrombus formation and pulmonary artery aneurysm in BD are very rare. The treatment protocol in patients with vascular involvement, particularly those with pulmonary artery aneurysm accompanied by thrombosis, have not been clearly defined. In this article, we report an exceptional case, who had been treated unsuccessfully with a combination of anti-inflammatory/immunosuppressive therapy and thrombolytic agents, to discuss the poor prognosis of pulmonary artery aneurysm accompanying intracardiac thrombosis in juvenile BD. Keywords: Behget's disease, intracardiac thrombosis, pulmonary artery aneurysm.
ISSN:2148-5046
2618-6500
DOI:10.5606/ArchRheumatol.2019.7169