Apert Syndrome: An Insight Into Dentofacial Features

Apert syndrome is a developmental malformation characterised by craniosynostosis (premature fusion of cranial sutures), midface hypoplasia, and syndactyly of hands and feet. Early synostosis of the coronal suture, cranial base, as well as agenesis of the sagittal suture, result in characteristic app...

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Bibliographic Details
Published in:Curēus (Palo Alto, CA) CA), 2021-09, Vol.13 (9)
Main Authors: Jose, Bijimole, Emmatty, Tharian B, Methippara, John Joseph, Kumar, Kavita, Thampi, Nidhi Mary
Format: Article
Language:English
Subjects:
Medical Education
Other
Quality Improvement
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Summary:Apert syndrome is a developmental malformation characterised by craniosynostosis (premature fusion of cranial sutures), midface hypoplasia, and syndactyly of hands and feet. Early synostosis of the coronal suture, cranial base, as well as agenesis of the sagittal suture, result in characteristic appearance and dental features like maxillary transverse and sagittal hypoplasia with concomitant dental crowding, a pseudo-cleft palate, and skeletal and dental anterior open bite. In this report, we discuss a case of Apert syndrome, with special emphasis on craniofacial characteristics, a multidisciplinary approach to its treatment, and the dentist’s role in management.
ISSN:2168-8184
2168-8184
DOI:10.7759/cureus.17735