Age-related changes in behavioural and emotional problems in Smith–Magenis syndrome measured with the Developmental Behavior Checklist

Smith–Magenis syndrome (SMS) is a genetic syndrome most often caused by a deletion on chromosome 17 or more rarely by a mutation in the retinoic acid-induced 1 gene. The aim of this study was to investigate the Developmental Behavior Checklist (DBC) profile of persons with SMS and the associations b...

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Published in:Journal of intellectual disabilities 2021-12, Vol.25 (4), p.429-440
Main Authors: Nag, Heidi Elisabeth, Nærland, Terje
Format: Article
Language:English
Subjects:
Adaptive behavior
Age Differences
Age groups
Antisocial Behavior
Anxiety
Autism
Behavior
Behavior change
Behavior disorders
Behavior Problems
Checklists
Chromosomes
Developmental disabilities
Emotional disorders
Emotional disturbances
Emotional Problems
Foreign Countries
Gender Differences
Genetic Disorders
Intellectual disabilities
Interpersonal Communication
Interpersonal Relationship
Pervasive Developmental Disorders
Symptoms (Individual Disorders)
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creator Nag, Heidi Elisabeth
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description Smith–Magenis syndrome (SMS) is a genetic syndrome most often caused by a deletion on chromosome 17 or more rarely by a mutation in the retinoic acid-induced 1 gene. The aim of this study was to investigate the Developmental Behavior Checklist (DBC) profile of persons with SMS and the associations between behavioural and emotional problems, age, gender, adaptive behaviour and autism symptomatology. Twenty-eight persons with SMS were represented by their parents in this study. DBC Total scores are reduced with age, but they still show a mean that is clearly above the cut-off of 46. The differences between the age groups
doi_str_mv 10.1177/1744629519901056
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source Applied Social Sciences Index & Abstracts (ASSIA); NORA - Norwegian Open Research Archives; ERIC; Sage Journals Online
subjects Adaptive behavior
Age Differences
Age groups
Antisocial Behavior
Anxiety
Autism
Behavior
Behavior change
Behavior disorders
Behavior Problems
Checklists
Chromosomes
Developmental disabilities
Emotional disorders
Emotional disturbances
Emotional Problems
Foreign Countries
Gender Differences
Genetic Disorders
Intellectual disabilities
Interpersonal Communication
Interpersonal Relationship
Pervasive Developmental Disorders
Symptoms (Individual Disorders)
title Age-related changes in behavioural and emotional problems in Smith–Magenis syndrome measured with the Developmental Behavior Checklist
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