The Epidemiology of Persons Living with Fontan in 2020 and Projections for 2030: Development of an Epidemiology Model Providing Multinational Estimates

Introduction Fontan surgery is a palliative procedure performed in children with a functionally univentricular heart. Improvements in surgical technique over the past 30 years have increased life expectancy in this rare population. However, the epidemiology of persons living with Fontan is poorly un...

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Bibliographic Details
Published in:Advances in therapy 2022-02, Vol.39 (2), p.1004-1015
Main Authors: Plappert, Leandra, Edwards, Susan, Senatore, Assunta, De Martini, Angela
Format: Article
Language:English
Subjects:
Adolescent
Adult
Cardiology
Child
Endocrinology
Fontan Procedure - adverse effects
Fontan Procedure - methods
Heart Defects, Congenital - epidemiology
Heart Defects, Congenital - surgery
Humans
Internal Medicine
Medicine
Medicine & Public Health
Oncology
Original Research
Pharmacology/Toxicology
Pulmonary Artery - surgery
Rheumatology
Survival Rate
Treatment Outcome
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Summary:Introduction Fontan surgery is a palliative procedure performed in children with a functionally univentricular heart. Improvements in surgical technique over the past 30 years have increased life expectancy in this rare population. However, the epidemiology of persons living with Fontan is poorly understood. This study aimed to estimate the 2020 and 2030 prevalence of persons living with a Fontan circulation in 11 countries across the US, Europe, Australia and New Zealand, by procedure type: [atriopulmonary connection (AP), lateral tunnel total cavopulmonary connection (LT-TCPC) or extracardiac total cavopulmonary connection (EC-TCPC)]; and age group: [children (
ISSN:0741-238X
1865-8652
DOI:10.1007/s12325-021-02002-3