Oligodontia of the permanent dentition in two sisters with polycystic ovarian syndrome: Case reports

Oligodontia or severe hypodontia is a rare developmental dental anomaly commonly associated with syndromes and systemic abnormalities. This report presents two sisters, aged 18 and 21, who collectively had 56 congenitally missing permanent teeth. Both patients exhibited pubertal hirsutism, menstrual...

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Published in:Oral surgery, oral medicine, oral pathology, oral radiology and endodontics oral medicine, oral pathology, oral radiology and endodontics, 1997-10, Vol.84 (4), p.368-371
Main Authors: Hattab, Faiez N, Angmar-Månsson, Birgit
Format: Article
Language:English
Subjects:
Adolescent
Adult
Anodontia - diagnosis
Anodontia - genetics
Anodontia - pathology
Anodontia - rehabilitation
Biological and medical sciences
Dentistry
Denture, Partial, Removable
Facial bones, jaws, teeth, parodontium: diseases, semeiology
Female
Hirsutism - pathology
Humans
Medical sciences
Medicin och hälsovetenskap
Menstruation Disturbances - pathology
Non tumoral diseases
Otorhinolaryngology. Stomatology
Polycystic Ovary Syndrome - diagnosis
Polycystic Ovary Syndrome - drug therapy
Polycystic Ovary Syndrome - genetics
Polycystic Ovary Syndrome - pathology
Puberty
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Summary:Oligodontia or severe hypodontia is a rare developmental dental anomaly commonly associated with syndromes and systemic abnormalities. This report presents two sisters, aged 18 and 21, who collectively had 56 congenitally missing permanent teeth. Both patients exhibited pubertal hirsutism, menstrual disturbances, and enlarged ovaries with multicystic lesions defined ultrasonically. These features are consistent with the diagnosis of polycystic ovarian syndrome, a disease not previously linked to hypodontia. A genetic component of this condition is proposed. The significance of this entity is discussed and the importance of early diagnosis and treatment regimens are emphasized.
ISSN:1079-2104
1528-395X
DOI:10.1016/S1079-2104(97)90034-2