DENTAL CARE OF PATIENTS WITH AICARDI SYNDROME: A CASE REPORT

• Published in: Oral surgery, oral medicine, oral pathology and oral radiology oral medicine, oral pathology and oral radiology, 2020-09, Vol.130 (3), p.e149-e149
• Main Authors: OLIVEIRA, GABRIELLA ALVES QUIXABEIRA, NUNES, FERNANDA FERREIRA, ARANTES, DIEGO ANTONIO COSTA, COSTA, NÁDIA DO LAGO, BÉRGAMO, NÁDIA APARECIDA, CAMPOS, CERISE DE CASTRO
• Format: Article
• Language: English
• ISSN: 2212-4403; 2212-4411
• DOI: 10.1016/j.oooo.2020.04.187

Aicardi syndrome does not have an etiology defined, linked to the X chromosome. The triad of infantile convulsions, agenesis of the corpus callosum, and chorioretinal gaps are important for the diagnosis. A patient diagnosed with Aicardi syndrome, female, aged 19, has had controlled convulsions for 6 years and presented with a complaint of teeth sensitivity, anterior open bite, and loss of elements 16 and 46. The molars erupted with brownish pigmentation, and the incisors and canines show signs of enamel hypoplasia. The panoramic radiography showed asymmetry in the heads of the mandible. The tooth 11 presented radicular dilaceration, and the teeth 45 and 35 are rotated. The clinical findings evaluated together favor the hypothesis of molar and incisor hypomineralization, enamel hypoplasia, and congenital syphilis. The patient showed motor coordination and was cooperative, allowing oral hygiene instruction techniques, photographic record, restorative procedures, and exodontia. The clinical follow-up of the patient is being performed every 4 months.