Giant thoracic ganglioneuroma with lymph node infiltration of a child: a case report

Background Ganglioneuroma is a rare neurogenic tumor which could grow into massive size in the thorax with minimal or no symptoms. Resection of these tumors will be challenging in view of large size and vascular encasement. Here, we report resection of a thoracic ganglioneuroma in a child with infil...

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Bibliographic Details
Published in:Annals of pediatric surgery 2020-12, Vol.16 (1), p.54-4, Article 54
Main Authors: Hettiarachchi, Mathula, Dharmadasa, Chanuka, Wijeyananda, Ashoka, Hettiarachchi, Kapila, Samarasinghe, Bandula
Format: Article
Language:English
Subjects:
Case Reports
Child
Consent
Coronary vessels
Histology
Lymph node
Lymphatic system
Magnetic resonance imaging
Medical diagnosis
Medical prognosis
Medicine
Medicine & Public Health
Metastasis
Neuroblastoma
Neurogenic tumors
Ostomy
Pediatrics
Surgery
Thoracic ganglioneuroma
Thoracic mass
Thorax
Tumors
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Summary:Background Ganglioneuroma is a rare neurogenic tumor which could grow into massive size in the thorax with minimal or no symptoms. Resection of these tumors will be challenging in view of large size and vascular encasement. Here, we report resection of a thoracic ganglioneuroma in a child with infiltration of spinal canal and lymph node metastasis, which is a very rare occurrence. Case presentation A 3-year and 10-month-old girl presented with a left side thoracic mass with minimal symptoms and signs. After the initial imaging with ultrasound scan and cross-sectional imaging, she had a true cut biopsy of the lesion confirming the diagnosis of ganglioneuroma. On exploration, she had a paraspinal thoracic mass extending from level of arch of aorta down to diaphragm with evidence of tumor infiltration of the intercostal spaces and spinal canal in multiple vertebral levels. Pathologically, she had infiltrated lymph nodes which were encircling the lower thoracic aorta. The tumor was resected successfully, and she recovered with a good functional status. Conclusion Thoracic ganglioneuroma has a good prognosis after complete resection even with spinal canal and lymph node infiltration. The resection could be arduous in case of massive size and vascular encasement; hence, benefit versus risk of complete resection should be carefully weighed.
ISSN:2090-5394
1687-4137
2090-5394
DOI:10.1186/s43159-020-00066-4