Case Report: A Giant Epignathus with a Well-Developed Skeleton of Head and Neck

Epignathus is an extremely rare teratoma found in the oral cavity or oropharyngeal region of newborns, whose pathogenesis is poorly understood. We describe a giant epignathus arising from the oropharynx in a newborn. The giant tumor completely obstructed the airway of the newborn resulting in death....

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Bibliographic Details
Published in:International journal of surgical pathology 2023-10, Vol.31 (7), p.1335-1339
Main Authors: Goto, Shintaro, Nakazawa, Atsuko, Yoshizawa, Tadashi, Aoki, Masahiko, Hirabayashi, Takeshi, Seino, Hiroko, Morohashi, Satoko, Kijima, Hiroshi
Format: Article
Language:English
Subjects:
Case reports
Newborn babies
Tumors
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Summary:Epignathus is an extremely rare teratoma found in the oral cavity or oropharyngeal region of newborns, whose pathogenesis is poorly understood. We describe a giant epignathus arising from the oropharynx in a newborn. The giant tumor completely obstructed the airway of the newborn resulting in death. Histological and radiological examination of the tumor reveals the presence of a remarkably well-developed skeleton of the head and neck. A row of teeth, the axis and atlas, thyroid and salivary glands, trachea, and cerebral tissue are all detected within the tumor. These findings suggest that the epignathus is fetus-in-fetu which is considered a type 0 germ cell tumor in accordance with current literature.
ISSN:1066-8969
1940-2465
DOI:10.1177/10668969221133739