Surgical treatment of scoliosis in patients with osteogenesis imperfecta: a single institution case series

Background Osteogenesis imperfecta (OI) is a connective tissue disorder characterized by skeletal deformities, bone fragility, and spinal complications. Various studies' insights underscored the impact of scoliosis on pulmonary function, positive outcomes with spinal fusion, and improved functi...

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Bibliographic Details
Published in:Musculoskeletal surgery 2024-12, Vol.108 (4), p.437-441
Main Authors: Chehrassan, M., Shakeri, M., Nikouei, F., Jafari, B., Mahabadi, E. A., Ghandhari, H.
Format: Article
Language:English
Subjects:
Adolescent
Adult
Child
Female
Follow-Up Studies
Humans
Male
Medicine
Medicine & Public Health
Original Article
Orthopedics
Osteogenesis Imperfecta - complications
Osteogenesis Imperfecta - surgery
Osteotomy - methods
Pedicle Screws
Postoperative Complications - etiology
Retrospective Studies
Scoliosis
Scoliosis - complications
Scoliosis - etiology
Scoliosis - surgery
Spinal Fusion - methods
Surgical Orthopedics
Treatment Outcome
Young Adult
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Summary:Background Osteogenesis imperfecta (OI) is a connective tissue disorder characterized by skeletal deformities, bone fragility, and spinal complications. Various studies' insights underscored the impact of scoliosis on pulmonary function, positive outcomes with spinal fusion, and improved functional abilities post-surgery. However, partial loss of correction remains inevitable. Methods This study examines six surgically treated OI patients with scoliosis. Surgical intervention using a posterior approach with pedicle screws and hooks aimed to correct spinal deformities. Preoperative, postoperative, and follow-up radiological assessments were conducted, revealing significant reductions in scoliotic angles post-surgery. Results Complications included infections and proximal junctional kyphosis requiring revision surgeries. Despite the challenges posed by poor bone quality and implant stability, no implant failures occurred in this series. Ponte osteotomies at the apex of deformity aided in corrective maneuvers. Conclusion Surgical treatment of scoliosis in patients affected by OI is challenging and may be associated with perioperative and postoperative complications. Ponte osteotomy may improve the correction and reduce necessary force at the time of correction.
ISSN:2035-5106
2035-5114
2035-5114
DOI:10.1007/s12306-024-00842-0