Butterfly-shaped pigment dystrophy of the fovea associated with subretinal neovascularization

The association of butterfly-shaped pigment dystrophy of the fovea, an uncommon inherited macular disease, with subretinal neovascularization has rarely been reported in the literature. We describe the clinical history of a patient affected with butterfly-shaped pigment dystrophy of the fovea, myopi...

Full description

Saved in:
Bibliographic Details
Published in:Graefe's archive for clinical and experimental ophthalmology 1996-04, Vol.234 (4), p.270-274
Main Authors: MARANO, F, DEUTMAN, A. F, AANDEKERK, A. L
Format: Article
Language:English
Subjects:
Angiography
Biological and medical sciences
Child, Preschool
Female
Fluorescein Angiography
Fovea Centralis
Humans
Medical sciences
Neovascularization, Pathologic - complications
Neovascularization, Pathologic - diagnosis
Ophthalmology
Retinal Diseases - complications
Retinal Diseases - diagnosis
Retinal Diseases - genetics
Retinal Vessels
Retinopathies
Television
Visual Acuity
Citations: Items that this one cites
Items that cite this one
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:The association of butterfly-shaped pigment dystrophy of the fovea, an uncommon inherited macular disease, with subretinal neovascularization has rarely been reported in the literature. We describe the clinical history of a patient affected with butterfly-shaped pigment dystrophy of the fovea, myopia, and optic nerve head dysplasia. She was followed up for 23 years. During the course of the disease, bilateral subretinal neovascularization in the macular area occurred. Fluorescein angiography confirmed the diagnosis. Recently, indocyanine green (CG) videoangiography was also performed. Because of the bilateral subfoveal localization no laser treatment was advised. Usually, good visual acuity is maintained in this uncommon inherited macular disease. However, acute visual loss can be caused by the ingrowth of subretinal new vessels. Therefore, if visual acuity decreases or metamorphopsia develops in these patients, careful biomicroscopic examination and fluorescein/ICG angiography is advisable.
ISSN:0721-832X
1435-702X
DOI:10.1007/BF00430421