Frantz's tumor: Is mutilating surgery always justified in young patients?

Abstract Background Solid pseudopapillary tumor (Frantz's tumor) of the pancreas is a rare lesion. It is of low-grade malignancy but can cause extensive local invasion. The aim of this study was to assess the outcome of Frantz's tumors after incomplete resection. Methods We contacted all a...

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Bibliographic Details
Published in:Surgical oncology 2011-06, Vol.20 (2), p.121-125
Main Authors: Campanile, M, Nicolas, A, LeBel, S, Delarue, A, Guys, J.M, de Lagausie, P
Format: Article
Language:English
Subjects:
Carcinoma, Papillary - diagnosis
Carcinoma, Papillary - surgery
Child
Female
Follow up
Frantz's tumor
Hematology, Oncology and Palliative Medicine
Humans
Pancreas
Pancreatic Neoplasms - diagnosis
Pancreatic Neoplasms - surgery
Postoperative Complications
Recurrence
Solid-pseudopapillary
Surgery
Treatment Outcome
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Summary:Abstract Background Solid pseudopapillary tumor (Frantz's tumor) of the pancreas is a rare lesion. It is of low-grade malignancy but can cause extensive local invasion. The aim of this study was to assess the outcome of Frantz's tumors after incomplete resection. Methods We contacted all authors who published case reports describing incomplete resection of Frantz's tumor between 1985 and 2008 to request follow-up information. Results Follow-up information was obtained for 11 out 18 patients who underwent incomplete resection. Estimated median survival rate was 5.7 years (69.5 months). Conclusion Since Frantz's tumor typically develops mainly in children and young women, a 5.7 year survival rate is unacceptable. Thus complete resection of locally invasive solid-pseudopapillary tumor of the pancreas is always justified, even at the price of difficult, mutilating surgery.
ISSN:0960-7404
1879-3320
DOI:10.1016/j.suronc.2009.12.003